๐Ÿฆต Section 716.5 ยท Congenital Angular Deformities of the Tibia and Fibula

Nelson Textbook of Pediatrics 22nd Edition | Posteromedial tibial bowing: benign, associated with calcaneovalgus foot, leg-length discrepancy ~4 cm. Anteromedial bowing: fibular hemimelia, equinocavovarus foot, tarsal coalition. Anterolateral bowing: congenital pseudarthrosis of tibia (CPT), associated with neurofibromatosis type 1 (50-60%), very difficult to treat. Management: observation, limb lengthening, amputation, vascularized fibular graft.

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๐Ÿ“‹ 30 Clinical Scenarios โ€” Congenital Angular Deformities of Tibia/Fibula

๐Ÿ“‡ Highโ€‘Yield Review Cards

๐Ÿฉบ Clinical Recognition: Congenital Tibial/Fibular Deformities

Select a presentation to review diagnostic clues and management per Nelson 716.5.

๐Ÿ“‹ Stepwise Management of Congenital Tibial/Fibular Deformities

๐Ÿ”‘ Key Principles โ€” Nelson Section 716.5
โ€ข Posteromedial tibial bowing: Benign. Associated with calcaneovalgus foot. Angulation corrects with growth. Mean LLD ~4 cm at maturity. Manage LLD with epiphysiodesis or lengthening.
โ€ข Anteromedial bowing (fibular hemimelia): Most common cause. Associated with femoral shortening, genu valgum, patellar instability, absent lateral rays, equinocavovarus foot, tarsal coalition. Treatment: foot reconstruction vs Syme/Boyd amputation.
โ€ข Anterolateral bowing: Congenital pseudarthrosis of tibia (CPT). Associated with neurofibromatosis type 1 (50-60%). Paley classification. Very difficult to union. Treatment: bracing, vascularized fibular graft, IM nailing, circular frame, or below-knee amputation.

    โšก Reflex Prompts โ€” Clinical Decisions

    ๐Ÿ“– Summary: Congenital Angular Deformities of Tibia & Fibula (Nelson 716.5)