🧬 Agammaglobulinemia (166.1)

Nelson Textbook of Pediatrics 22nd Edition — X-linked agammaglobulinemia (XLA, Bruton disease), autosomal recessive agammaglobulinemia (μ heavy chain, Igα, Igβ, BLNK, etc.), absent B cells, profound hypogammaglobulinemia, recurrent sinopulmonary infections, enteroviral encephalitis, IVIG replacement