📘 Defects in the β-Oxidation Cycle

Nelson Textbook of Pediatrics 22nd Ed — Section 106.1. MCAD (ACADM), VLCAD (ACADVL), LCHAD/MTP (HADHA/HADHB), SCAD (ACADS), SCHAD (HADH). Hypoketotic hypoglycemia, cardiomyopathy, rhabdomyolysis, acylcarnitine patterns. Emergency: IV glucose, carnitine, triheptanoin.

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📋 30 Clinical Scenarios — β-Oxidation Cycle Defects (FCPS level)

📇 High‑Yield Review Cards (β-Oxidation Cycle)

🩺 Symptom‑Based Approach: β-Oxidation Defects

Select a presentation for diagnostic clues.

📋 Emergency & Long-term Management of β-Oxidation Defects

    ⚡ Reflex Prompts — Clinical Decisions in β-Oxidation Disorders

    📖 Summary: β-Oxidation Cycle Defects — Nelson 22nd Ed