📘 Muscle Glycogenoses · GSD II, V, VII, III, Danon, PRKAG2

Nelson Textbook of Pediatrics 22nd Ed — Section 107.1. GSD II (Pompe): cardiomyopathy, hypotonia, ERT. GSD V (McArdle): exercise intolerance, cramps, second-wind phenomenon. GSD VII (Tarui): similar + hemolysis. GSD III: muscle weakness. Danon disease: X-linked cardiomyopathy, intellectual disability.

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📋 30 Clinical Scenarios — Muscle Glycogenoses (FCPS level)

📇 High‑Yield Review Cards (Muscle Glycogenoses)

🩺 Symptom‑Based Approach: Muscle Glycogenoses

Select a presentation for diagnostic clues.

📋 Management of Muscle Glycogenoses

    ⚡ Reflex Prompts — Clinical Decisions in Muscle GSD

    📖 Summary: Muscle Glycogenoses — Nelson 22nd Ed