🧬 646.3 · Syringomyelia

Nelson Textbook of Pediatrics 22nd Edition | CSF-filled cavity (syrinx) within the spinal cord. Most commonly associated with Chiari I malformation. Also caused by trauma, tumor, arachnoiditis, idiopathic. Clinical: dissociated sensory loss (loss of pain/temperature, preserved vibration/proprioception – cape-like distribution), weakness, areflexia, scoliosis, neurogenic bladder. Diagnosis: MRI spine. Treatment: treat underlying cause (posterior fossa decompression for Chiari I). Syrinx shunting rarely needed. Asymptomatic syrinx may be observed.

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πŸ“‹ 30 Clinical Scenarios β€” Syringomyelia (Pediatric Neurology/Neurosurgery)

πŸ“‡ High‑Yield Review Cards: Syringomyelia

🩺 Symptom‑Based Diagnostic Approach (Syringomyelia)

Select a presentation for diagnostic clues and management.

πŸ“‹ Stepwise Management of Syringomyelia

    ⚑ Reflex Prompts β€” Critical Decisions in Syringomyelia

    πŸ“– Summary: Syringomyelia β€” Nelson 22nd Ed