💊 Section 686.2: Multisystem Medication Reactions

Nelson Textbook of Pediatrics 22nd Edition | Severe cutaneous adverse reactions (SCARs) — DRESS syndrome (drug rash with eosinophilia and systemic symptoms), serum sickness‑like reaction (SSLR), acute generalized exanthematous pustulosis (AGEP), fixed drug eruption (FDE). Recognition, culprit drugs, and stepwise management.

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📋 30 Clinical Scenarios — DRESS, SSLR, AGEP, Fixed Drug Eruption

📇 High‑Yield Review Cards | Medication Reactions

🩺 Clinical Presentation → Differential Diagnosis

Select a presentation to identify the likely drug reaction and management steps.

📋 Stepwise Approach to Severe Cutaneous Adverse Reactions (SCARs)

🔑 Key Principles — Nelson 686.2
DRESS (DIHS): onset 2‑6 weeks after drug; fever, rash (morbilliform → erythroderma), facial edema, lymphadenopathy, eosinophilia, atypical lymphocytosis, hepatitis, nephritis, pneumonitis, myocarditis. Mortality ~10%. Latent HHV‑6 reactivation.
Serum sickness‑like reaction (SSLR): 10‑14 days after drug (cephalosporins, penicillins, minocycline). Urticarial/annular plaques with violaceous center, fever, arthralgia, lymphadenopathy. NO immune complexes (unlike true serum sickness).
AGEP: hours to days after drug (aminopenicillins, macrolides). Fever, dozens of nonfollicular sterile pustules on edematous erythema, intertriginous onset, desquamation. Neutrophilia.
Fixed drug eruption (FDE): minutes to hours after drug; solitary or few round dusky red/violaceous patches, recur at same site upon re‑exposure. Resolves with hyperpigmentation.

    ⚡ Reflex Prompts — Clinical Decisions

    📖 Summary: Multisystem Medication Reactions (Nelson 686.2)